Disfuncție bactericidă a fagocitelor
Tulburări în care celulele fagocitare nu pot distruge bacteriile ingerate; se caracterizează prin infecții frecvente recurente și formarea de granuloame.
Forme specifice incluse
Include 8 subtipuri înrudite ↓Ascunde subtipurile ↑
- chronic granulomatous disease
- granulomatous disease with defect in neutrophil chemotaxis
- granulomatous disease, chronic, autosomal recessive, 5
- granulomatous disease, chronic, autosomal recessive, cytochrome b-negative
- granulomatous disease, chronic, autosomal recessive, cytochrome b-positive, type 1
- granulomatous disease, chronic, autosomal recessive, cytochrome b-positive, type 2
- granulomatous disease, chronic, autosomal recessive, cytochrome b-positive, type 3
- granulomatous disease, chronic, X-linked
