Heritable Pulmonary Arterial Hypertension
Heritable pulmonary arterial hypertension (HPAH) is a form of pulmonary arterial hypertension (PAH), occurring due to mutations in PAH predisposing genes or in a familial context. HPAH is characterized by elevated pulmonary arterial resistance leading to right heart failure. HPAH is progressive and potentially fatal.
Más néven
familial pulmonary arterial hypertension; FPAH; hereditary pulmonary arterial hypertension; HPAH
7 kapcsolódó altípust tartalmaz ↓Altípusok elrejtése ↑
- pulmonary hypertension, primary, 1
- pulmonary hypertension, primary, 2
- pulmonary hypertension, primary, 3
- pulmonary hypertension, primary, 4
- pulmonary hypertension, primary, 5
- pulmonary hypertension, primary, 6
- pulmonary hypertension, primary, 7
